The diagnosis of HPS depends on establishing that impaired gas exchange in a patient with liver disease is due to pulmonary vascular dilatation. In most cases, the results of arterial blood gases and ...

Previously in the Journal, we reported on a 4-year-old boy with the hepatopulmonary syndrome, a condition characterized by intrapulmonary shunting due to dilatation of pulmonary vessels in the setting ...

We recently described the TEMPI syndrome (Aug. 4, 2011), 1 which is characterized by the pentad of telangiectasias, elevated erythropoietin level and erythrocytosis, monoclonal gammopathy, perinephric ...

The characteristics of hepatopulmonary syndrome include an oxygen saturation < 80%, an increased alveolar-arterial gradient (> 15 mm Hg) while breathing room air, portal hypertension with or without ...